Fatal bleeding following delivery: a manifestation of the vascular type of Ehlers-Danlos' syndrome
2007 (English)In: Gynecologic and Obstetric Investigation, ISSN 0378-7346, E-ISSN 1423-002x, Vol. 63, no 3, 173-175 p.Article in journal (Refereed) Published
Introduction: The vascular form of Ehlers-Danlos' syndrome (type IV) is a potentially lethal genetic condition because of rupture of major arteries, often in the peri-partum period. Case Report: We report a 31-year-old primipara who died from a rupture of the right subclavian artery. The patient had several symptoms and signs typical of the disease. The rupture occurred during the expulsion-phase of delivery but was recognized only on day 9. Conclusion: Early recognition is crucial to avoid maternal mortality due to this genetic disorder. Once the condition is suspected, the clinical diagnosis is straightforward.
Place, publisher, year, edition, pages
2007. Vol. 63, no 3, 173-175 p.
Ehlers-Danlos' syndrome, Subclavian artery, Delivery, Bleeding, Rupture
Medical and Health Sciences
IdentifiersURN: urn:nbn:se:uu:diva-11669DOI: 10.1159/000097659ISI: 000244746900013PubMedID: 17139178OAI: oai:DiVA.org:uu-11669DiVA: diva2:39438