uu.seUppsala University Publications
Change search
ReferencesLink to record
Permanent link

Direct link
A long term follow up of 15 patients with arrhythmogenic right ventricular dysplasia
Uppsala University, Disciplinary Domain of Medicine and Pharmacy, Faculty of Medicine, Department of Medical Sciences. (Cardiology-arrhythmia)
1987 (English)In: British Heart Journal, ISSN 0007-0769, Vol. 58, no 5, 477-488 p.Article in journal (Refereed) Published
Abstract [en]

The clinical course in 15 patients with features consistent with arrhythmogenic right ventricular dysplasia is described. At referral seven patients had abnormal physical findings, nine had abnormal electrocardiograms with non-specific right-sided abnormalities, and seven patients had increased heart size or prominent right ventricles on chest x ray. During long term follow up (mean 8.8 years, range 1.5 to 28 years) 11 patients had abnormal physical findings, 11 had electrocardiographic changes, and nine had increased heart size. Recurrent sustained right ventricular tachycardia was the most common arrhythmia (10 patients). Two patients experienced ventricular fibrillation. Seven patients suffered from over 10 episodes of ventricular tachycardia, nine required cardioversions, and 10 patients had associated serious symptoms such as syncope, severe hypotension, or cardiac arrest. Four patients required operation to correct the arrhythmia and three patients developed right heart failure. Two out of three deaths were sudden. These data suggest that in arrhythmogenic right ventricular dysplasia right ventricular abnormalities may be progressive and that the condition may affect the left ventricle. The course of the ventricular arrhythmias was highly variable and could not be predicted in individual patients. The potential for lethal ventricular arrhythmias is evident and warrants intensive diagnostic efforts to identify patients with adverse prognostic features.

Place, publisher, year, edition, pages
1987. Vol. 58, no 5, 477-488 p.
Keyword [en]
Adolescent, Adult, Anti-Arrhythmia Agents/therapeutic use, Cardiomyopathies/*diagnosis/physiopathology, Child, Electrocardiography, Female, Follow-Up Studies, Heart Ventricles, Humans, Male, Middle Aged, Prognosis, Recurrence, Research Support; Non-U.S. Gov't, Syndrome, Tachycardia/*diagnosis/physiopathology/prevention & control
National Category
Medical and Health Sciences
URN: urn:nbn:se:uu:diva-69374PubMedID: 3676037OAI: oai:DiVA.org:uu-69374DiVA: diva2:97285
Available from: 2005-03-31 Created: 2005-03-31 Last updated: 2010-06-04Bibliographically approved

Open Access in DiVA

No full text

Other links


Search in DiVA

By author/editor
Blomström-Lundqvist, C
By organisation
Department of Medical Sciences
Medical and Health Sciences

Search outside of DiVA

GoogleGoogle Scholar
The number of downloads is the sum of all downloads of full texts. It may include eg previous versions that are now no longer available

Altmetric score

Total: 127 hits
ReferencesLink to record
Permanent link

Direct link